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A physician survey reveals differences in management of idiopathic pulmonary hemosiderosis.

Identifieur interne : 000F09 ( Main/Exploration ); précédent : 000F08; suivant : 000F10

A physician survey reveals differences in management of idiopathic pulmonary hemosiderosis.

Auteurs : Chana I C. Chin [États-Unis] ; Shirleen Loloyan Kohn [États-Unis] ; Thomas G. Keens [États-Unis] ; Monique F. Margetis [États-Unis] ; Roberta M. Kato [États-Unis]

Source :

RBID : pubmed:26289251

Descripteurs français

English descriptors

Abstract

Idiopathic pulmonary hemosiderosis (IPH) is a rare disorder of unknown etiology characterized by chronic pulmonary hemorrhage and presents with a triad of anemia, hemoptysis and pulmonary infiltrates. IPH is a diagnosis of exclusion with a variable and disparate clinical course. Despite existing therapies, few children achieve full remission while others have recurrent hemorrhage, progressive lung damage, and premature death.

DOI: 10.1186/s13023-015-0319-5
PubMed: 26289251


Affiliations:


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<div type="abstract" xml:lang="en">Idiopathic pulmonary hemosiderosis (IPH) is a rare disorder of unknown etiology characterized by chronic pulmonary hemorrhage and presents with a triad of anemia, hemoptysis and pulmonary infiltrates. IPH is a diagnosis of exclusion with a variable and disparate clinical course. Despite existing therapies, few children achieve full remission while others have recurrent hemorrhage, progressive lung damage, and premature death.</div>
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